SUCCINYLACETONE IS THE PRIMARY MARKER FOR DETECTION OF TYROSINEMIA TYPE 1 WHERE TYROSINE CONCENTRATION MAY OR MAY NOT BE ELEVATED. NORMAL LEVELS MAY BE SEEN IN AFFECTED INDIVIDUALS UNDERGOING TREATMENT.
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10 ML (5 ML MIN.) ALIQOUT OF RANDOM URINE IN A STERILE SCREW CAPPED CONTAINER. DO NOT USE PRESERVATIVES. SHIP REFRIGERATED OR FROZEN. GIVE BRIEF CLINICAL HISTORY.